Diagnostic Radiology/Musculoskeletal Imaging/Tumors Basic/Maffuci syndrome

Maffucci's syndrome is defined as multiple enchondromatosis with soft tissue and visceral hemangiomas. Patients with Maffucci's syndrome are believed to be at far greater risk for malignant transformation than those with Ollier's disease.



Fig. 1 Maffucci's syndrome. Soft tissue masses with phleboliths are consistent with hemangiomas. Note remodeling of underlying bone.